Ong T, Ramsey BW (September 2015). "Update in Cystic Fibrosis 2014". American Journal of Respiratory and Critical Care Medicine. 192 (6): 669–675. doi:10.1164/rccm.201504-0656UP. PMID26371812.
Flume PA, Mogayzel PJ, Robinson KA, Rosenblatt RL, Quittell L, Marshall BC (August 2010). "Cystic fibrosis pulmonary guidelines: pulmonary complications: hemoptysis and pneumothorax". American Journal of Respiratory and Critical Care Medicine. 182 (3): 298–306. doi:10.1164/rccm.201002-0157OC. PMID20675678.
Rowe SM, Miller S, Sorscher EJ (May 2005). "Cystic fibrosis". The New England Journal of Medicine. 352 (19): 1992–2001. doi:10.1056/NEJMra043184. PMID15888700.
Kulczycki LL, Shwachman H (August 1958). "Studies in cystic fibrosis of the pancreas; occurrence of rectal prolapse". The New England Journal of Medicine. 259 (9): 409–412. doi:10.1056/NEJM195808282590901. PMID13578072.
Assis DN, Freedman SD (March 2016). "Gastrointestinal Disorders in Cystic Fibrosis". Clinics in Chest Medicine (Review). 37 (1): 109–118. doi:10.1016/j.ccm.2015.11.004. PMID26857772.
Lamireau T, Monnereau S, Martin S, Marcotte JE, Winnock M, Alvarez F (December 2004). "Epidemiology of liver disease in cystic fibrosis: a longitudinal study". Journal of Hepatology. 41 (6): 920–925. doi:10.1016/j.jhep.2004.08.006. PMID15582124.
Williams SG, Westaby D, Tanner MS, Mowat AP (October 1992). "Liver and biliary problems in cystic fibrosis". British Medical Bulletin. 48 (4): 877–892. doi:10.1093/oxfordjournals.bmb.a072583. PMID1458306.
McCallum TJ, Milunsky JM, Cunningham DL, Harris DH, Maher TA, Oates RD (October 2000). "Fertility in men with cystic fibrosis: an update on current surgical practices and outcomes". Chest. 118 (4): 1059–1062. doi:10.1378/chest.118.4.1059. PMID11035677.
Augarten A, Yahav Y, Kerem BS, Halle D, Laufer J, Szeinberg A, et al. (November 1994). "Congenital bilateral absence of vas deferens in the absence of cystic fibrosis". Lancet. 344 (8935): 1473–1474. doi:10.1016/S0140-6736(94)90292-5. PMID7968122. S2CID28860665.
Gilljam M, Antoniou M, Shin J, Dupuis A, Corey M, Tullis DE (July 2000). "Pregnancy in cystic fibrosis. Fetal and maternal outcome". Chest. 118 (1): 85–91. doi:10.1378/chest.118.1.85. PMID10893364. S2CID32289370.
Edwards QT, Seibert D, Macri C, Covington C, Tilghman J (November 2004). "Assessing ethnicity in preconception counseling: genetics--what nurse practitioners need to know". Journal of the American Academy of Nurse Practitioners. 16 (11): 472–480. doi:10.1111/j.1745-7599.2004.tb00426.x. PMID15617360. S2CID7644129.
Graeber SY, Mall MA (September 2023). "The future of cystic fibrosis treatment: from disease mechanisms to novel therapeutic approaches". Lancet. 402 (10408): 1185–1198. doi:10.1016/s0140-6736(23)01608-2. PMID37699417. S2CID261623275.
Schwiebert EM, Benos DJ, Egan ME, Stutts MJ, Guggino WB (January 1999). "CFTR is a conductance regulator as well as a chloride channel". Physiological Reviews. 79 (1 Suppl): S145–S166. doi:10.1152/physrev.1999.79.1.S145. PMID9922379.
Linsdell P (January 2006). "Mechanism of chloride permeation in the cystic fibrosis transmembrane conductance regulator chloride channel". Experimental Physiology. 91 (1): 123–129. doi:10.1113/expphysiol.2005.031757. PMID16157656. S2CID37254079.
Childers M, Eckel G, Himmel A, Caldwell J (2007). "A new model of cystic fibrosis pathology: lack of transport of glutathione and its thiocyanate conjugates". Medical Hypotheses. 68 (1): 101–112. doi:10.1016/j.mehy.2006.06.020. PMID16934416.
Verkman AS, Song Y, Thiagarajah JR (January 2003). "Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease". American Journal of Physiology. Cell Physiology. 284 (1): C2-15. doi:10.1152/ajpcell.00417.2002. PMID12475759. S2CID11790119.
Pankhurst CL, Philpott-Howard J (April 1996). "The environmental risk factors associated with medical and dental equipment in the transmission of Burkholderia (Pseudomonas) cepacia in cystic fibrosis patients". The Journal of Hospital Infection. 32 (4): 249–255. doi:10.1016/S0195-6701(96)90035-3. PMID8744509.
Høiby N (June 1995). "Isolation and treatment of cystic fibrosis patients with lung infections caused by Pseudomonas (Burkholderia) cepacia and multiresistant Pseudomonas aeruginosa". The Netherlands Journal of Medicine. 46 (6): 280–287. doi:10.1016/0300-2977(95)00020-N. PMID7643943.
Hoch H, Sontag MK, Scarbro S, Juarez-Colunga E, McLean C, Kempe A, et al. (November 2018). "Clinical outcomes in U.S. infants with cystic fibrosis from 2001 to 2012". Pediatric Pulmonology. 53 (11): 1492–1497. doi:10.1002/ppul.24165. PMID30259702. S2CID52845580.
Elias S, Annas GJ, Simpson JL (April 1991). "Carrier screening for cystic fibrosis: implications for obstetric and gynecologic practice". American Journal of Obstetrics and Gynecology. 164 (4): 1077–1083. doi:10.1016/0002-9378(91)90589-j. PMID2014829.
Tabor A, Philip J, Madsen M, Bang J, Obel EB, Nørgaard-Pedersen B (June 1986). "Randomised controlled trial of genetic amniocentesis in 4606 low-risk women". Lancet. 1 (8493): 1287–1293. doi:10.1016/S0140-6736(86)91218-3. PMID2423826. S2CID31237495.
Eddleman KA, Malone FD, Sullivan L, Dukes K, Berkowitz RL, Kharbutli Y, et al. (November 2006). "Pregnancy loss rates after midtrimester amniocentesis". Obstetrics and Gynecology. 108 (5): 1067–1072. doi:10.1097/01.AOG.0000240135.13594.07. PMID17077226. S2CID19081825.
Pai VB, Nahata MC (October 2001). "Efficacy and safety of aerosolized tobramycin in cystic fibrosis". Pediatric Pulmonology. 32 (4): 314–327. doi:10.1002/ppul.1125. PMID11568993. S2CID30108514.
Ryan G, Singh M, Dwan K (March 2011). "Inhaled antibiotics for long-term therapy in cystic fibrosis". The Cochrane Database of Systematic Reviews (3): CD001021. doi:10.1002/14651858.CD001021.pub2. PMID21412868.
Tan KH, Mulheran M, Knox AJ, Smyth AR (March 2003). "Aminoglycoside prescribing and surveillance in cystic fibrosis". American Journal of Respiratory and Critical Care Medicine. 167 (6): 819–823. doi:10.1164/rccm.200109-012CC. PMID12623858.
Langton Hewer SC, Smith S, Rowbotham NJ, Yule A, Smyth AR (June 2023). "Antibiotic strategies for eradicating Pseudomonas aeruginosa in people with cystic fibrosis". The Cochrane Database of Systematic Reviews. 2023 (6): CD004197. doi:10.1002/14651858.CD004197.pub6. PMC 10237531. PMID37268599.
Kuver R, Lee SP (April 2006). "Hypertonic saline for cystic fibrosis". The New England Journal of Medicine. 354 (17): 1848–51, author reply 1848–51. doi:10.1056/NEJMc060351. PMID16642591. S2CID26244542.
Lieberman J (July 1968). "Dornase aerosol effect on sputum viscosity in cases of cystic fibrosis". JAMA. 205 (5): 312–313. doi:10.1001/jama.205.5.312. PMID5694947.
Kellerman D, Rossi Mospan A, Engels J, Schaberg A, Gorden J, Smiley L (August 2008). "Denufosol: a review of studies with inhaled P2Y(2) agonists that led to Phase 3". Pulmonary Pharmacology & Therapeutics. 21 (4): 600–607. doi:10.1016/j.pupt.2007.12.003. PMID18276176.
Wilkinson GR (October 1996). "Cytochrome P4503A (CYP3A) metabolism: prediction of in vivo activity in humans". Journal of Pharmacokinetics and Biopharmaceutics. 24 (5): 475–490. doi:10.1007/BF02353475. PMID9131486. S2CID30289771.
Ferguson JH, Chang AB (May 2014). "Vitamin D supplementation for cystic fibrosis". The Cochrane Database of Systematic Reviews (5): CD007298. doi:10.1002/14651858.CD007298.pub4. PMID24823922.
Hardin DS, Rice J, Ahn C, Ferkol T, Howenstine M, Spears S, et al. (March 2005). "Growth hormone treatment enhances nutrition and growth in children with cystic fibrosis receiving enteral nutrition". The Journal of Pediatrics. 146 (3): 324–328. doi:10.1016/j.jpeds.2004.10.037. PMID15756212.
Hegarty M, Macdonald J, Watter P, Wilson C (July 2009). "Quality of life in young people with cystic fibrosis: effects of hospitalization, age and gender, and differences in parent/child perceptions". Child. 35 (4): 462–468. doi:10.1111/j.1365-2214.2008.00900.x. PMID18991968. Havermans T, Vreys M, Proesmans M, De Boeck C (January 2006). "Assessment of agreement between parents and children on health-related quality of life in children with cystic fibrosis". Child. 32 (1): 1–7. doi:10.1111/j.1365-2214.2006.00564.x. PMID16398786.
Moorcroft AJ, Dodd ME, Webb AK (1998). "Exercise limitations and training for patients with cystic fibrosis". Disability and Rehabilitation. 20 (6–7): 247–253. doi:10.3109/09638289809166735. PMID9637933.
Rosenstein BJ, Cutting GR (April 1998). "The diagnosis of cystic fibrosis: a consensus statement. Cystic Fibrosis Foundation Consensus Panel". The Journal of Pediatrics. 132 (4): 589–595. doi:10.1016/S0022-3476(98)70344-0. PMID9580754.
Wennberg C, Kucinskas V (1994). "Low frequency of the delta F508 mutation in Finno-Ugrian and Baltic populations". Human Heredity. 44 (3): 169–171. doi:10.1159/000154210. PMID8039801.
Kere J, Savilahti E, Norio R, Estivill X, de la Chapelle A (September 1990). "Cystic fibrosis mutation delta F508 in Finland: other mutations predominate". Human Genetics. 85 (4): 413–415. doi:10.1007/BF02428286. PMID2210753. S2CID38364780.
Gabriel SE, Brigman KN, Koller BH, Boucher RC, Stutts MJ (October 1994). "Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model". Science. 266 (5182): 107–109. Bibcode:1994Sci...266..107G. doi:10.1126/science.7524148. PMID7524148.
Alfonso-Sánchez MA, Pérez-Miranda AM, García-Obregón S, Peña JA (June 2010). "An evolutionary approach to the high frequency of the Delta F508 CFTR mutation in European populations". Medical Hypotheses. 74 (6): 989–992. doi:10.1016/j.mehy.2009.12.018. PMID20110149.
Tobacman JK (June 2003). "Does deficiency of arylsulfatase B have a role in cystic fibrosis?". Chest. 123 (6): 2130–2139. doi:10.1378/chest.123.6.2130. PMID12796199.
Di Sant'Agnese PA, Darling RC, Perera GA, Shea E (November 1953). "Abnormal electrolyte composition of sweat in cystic fibrosis of the pancreas; clinical significance and relationship to the disease". Pediatrics. 12 (5): 549–563. doi:10.1542/peds.12.5.549. PMID13111855. S2CID42514224.
Eiberg H, Mohr J, Schmiegelow K, Nielsen LS, Williamson R (October 1985). "Linkage relationships of paraoxonase (PON) with other markers: indication of PON-cystic fibrosis synteny". Clinical Genetics. 28 (4): 265–271. doi:10.1111/j.1399-0004.1985.tb00400.x. PMID2998653. S2CID41143417.
Riordan JR, Rommens JM, Kerem B, Alon N, Rozmahel R, Grzelczak Z, et al. (September 1989). "Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA". Science. 245 (4922): 1066–1073. Bibcode:1989Sci...245.1066R. doi:10.1126/science.2475911. PMID2475911. S2CID84566748.
Hanlon GW (August 2007). "Bacteriophages: an appraisal of their role in the treatment of bacterial infections". International Journal of Antimicrobial Agents. 30 (2): 118–128. doi:10.1016/j.ijantimicag.2007.04.006. PMID17566713.
Ong T, Ramsey BW (September 2015). "Update in Cystic Fibrosis 2014". American Journal of Respiratory and Critical Care Medicine. 192 (6): 669–675. doi:10.1164/rccm.201504-0656UP. PMID26371812.
Flume PA, Mogayzel PJ, Robinson KA, Rosenblatt RL, Quittell L, Marshall BC (August 2010). "Cystic fibrosis pulmonary guidelines: pulmonary complications: hemoptysis and pneumothorax". American Journal of Respiratory and Critical Care Medicine. 182 (3): 298–306. doi:10.1164/rccm.201002-0157OC. PMID20675678.
Rowe SM, Miller S, Sorscher EJ (May 2005). "Cystic fibrosis". The New England Journal of Medicine. 352 (19): 1992–2001. doi:10.1056/NEJMra043184. PMID15888700.
Kulczycki LL, Shwachman H (August 1958). "Studies in cystic fibrosis of the pancreas; occurrence of rectal prolapse". The New England Journal of Medicine. 259 (9): 409–412. doi:10.1056/NEJM195808282590901. PMID13578072.
Assis DN, Freedman SD (March 2016). "Gastrointestinal Disorders in Cystic Fibrosis". Clinics in Chest Medicine (Review). 37 (1): 109–118. doi:10.1016/j.ccm.2015.11.004. PMID26857772.
Lamireau T, Monnereau S, Martin S, Marcotte JE, Winnock M, Alvarez F (December 2004). "Epidemiology of liver disease in cystic fibrosis: a longitudinal study". Journal of Hepatology. 41 (6): 920–925. doi:10.1016/j.jhep.2004.08.006. PMID15582124.
Williams SG, Westaby D, Tanner MS, Mowat AP (October 1992). "Liver and biliary problems in cystic fibrosis". British Medical Bulletin. 48 (4): 877–892. doi:10.1093/oxfordjournals.bmb.a072583. PMID1458306.
McCallum TJ, Milunsky JM, Cunningham DL, Harris DH, Maher TA, Oates RD (October 2000). "Fertility in men with cystic fibrosis: an update on current surgical practices and outcomes". Chest. 118 (4): 1059–1062. doi:10.1378/chest.118.4.1059. PMID11035677.
Augarten A, Yahav Y, Kerem BS, Halle D, Laufer J, Szeinberg A, et al. (November 1994). "Congenital bilateral absence of vas deferens in the absence of cystic fibrosis". Lancet. 344 (8935): 1473–1474. doi:10.1016/S0140-6736(94)90292-5. PMID7968122. S2CID28860665.
Gilljam M, Antoniou M, Shin J, Dupuis A, Corey M, Tullis DE (July 2000). "Pregnancy in cystic fibrosis. Fetal and maternal outcome". Chest. 118 (1): 85–91. doi:10.1378/chest.118.1.85. PMID10893364. S2CID32289370.
Edwards QT, Seibert D, Macri C, Covington C, Tilghman J (November 2004). "Assessing ethnicity in preconception counseling: genetics--what nurse practitioners need to know". Journal of the American Academy of Nurse Practitioners. 16 (11): 472–480. doi:10.1111/j.1745-7599.2004.tb00426.x. PMID15617360. S2CID7644129.
Graeber SY, Mall MA (September 2023). "The future of cystic fibrosis treatment: from disease mechanisms to novel therapeutic approaches". Lancet. 402 (10408): 1185–1198. doi:10.1016/s0140-6736(23)01608-2. PMID37699417. S2CID261623275.
Schwiebert EM, Benos DJ, Egan ME, Stutts MJ, Guggino WB (January 1999). "CFTR is a conductance regulator as well as a chloride channel". Physiological Reviews. 79 (1 Suppl): S145–S166. doi:10.1152/physrev.1999.79.1.S145. PMID9922379.
Linsdell P (January 2006). "Mechanism of chloride permeation in the cystic fibrosis transmembrane conductance regulator chloride channel". Experimental Physiology. 91 (1): 123–129. doi:10.1113/expphysiol.2005.031757. PMID16157656. S2CID37254079.
Childers M, Eckel G, Himmel A, Caldwell J (2007). "A new model of cystic fibrosis pathology: lack of transport of glutathione and its thiocyanate conjugates". Medical Hypotheses. 68 (1): 101–112. doi:10.1016/j.mehy.2006.06.020. PMID16934416.
Verkman AS, Song Y, Thiagarajah JR (January 2003). "Role of airway surface liquid and submucosal glands in cystic fibrosis lung disease". American Journal of Physiology. Cell Physiology. 284 (1): C2-15. doi:10.1152/ajpcell.00417.2002. PMID12475759. S2CID11790119.
Pankhurst CL, Philpott-Howard J (April 1996). "The environmental risk factors associated with medical and dental equipment in the transmission of Burkholderia (Pseudomonas) cepacia in cystic fibrosis patients". The Journal of Hospital Infection. 32 (4): 249–255. doi:10.1016/S0195-6701(96)90035-3. PMID8744509.
Høiby N (June 1995). "Isolation and treatment of cystic fibrosis patients with lung infections caused by Pseudomonas (Burkholderia) cepacia and multiresistant Pseudomonas aeruginosa". The Netherlands Journal of Medicine. 46 (6): 280–287. doi:10.1016/0300-2977(95)00020-N. PMID7643943.
Hoch H, Sontag MK, Scarbro S, Juarez-Colunga E, McLean C, Kempe A, et al. (November 2018). "Clinical outcomes in U.S. infants with cystic fibrosis from 2001 to 2012". Pediatric Pulmonology. 53 (11): 1492–1497. doi:10.1002/ppul.24165. PMID30259702. S2CID52845580.
Elias S, Annas GJ, Simpson JL (April 1991). "Carrier screening for cystic fibrosis: implications for obstetric and gynecologic practice". American Journal of Obstetrics and Gynecology. 164 (4): 1077–1083. doi:10.1016/0002-9378(91)90589-j. PMID2014829.
Tabor A, Philip J, Madsen M, Bang J, Obel EB, Nørgaard-Pedersen B (June 1986). "Randomised controlled trial of genetic amniocentesis in 4606 low-risk women". Lancet. 1 (8493): 1287–1293. doi:10.1016/S0140-6736(86)91218-3. PMID2423826. S2CID31237495.
Eddleman KA, Malone FD, Sullivan L, Dukes K, Berkowitz RL, Kharbutli Y, et al. (November 2006). "Pregnancy loss rates after midtrimester amniocentesis". Obstetrics and Gynecology. 108 (5): 1067–1072. doi:10.1097/01.AOG.0000240135.13594.07. PMID17077226. S2CID19081825.
Pai VB, Nahata MC (October 2001). "Efficacy and safety of aerosolized tobramycin in cystic fibrosis". Pediatric Pulmonology. 32 (4): 314–327. doi:10.1002/ppul.1125. PMID11568993. S2CID30108514.
Ryan G, Singh M, Dwan K (March 2011). "Inhaled antibiotics for long-term therapy in cystic fibrosis". The Cochrane Database of Systematic Reviews (3): CD001021. doi:10.1002/14651858.CD001021.pub2. PMID21412868.
Tan KH, Mulheran M, Knox AJ, Smyth AR (March 2003). "Aminoglycoside prescribing and surveillance in cystic fibrosis". American Journal of Respiratory and Critical Care Medicine. 167 (6): 819–823. doi:10.1164/rccm.200109-012CC. PMID12623858.
Langton Hewer SC, Smith S, Rowbotham NJ, Yule A, Smyth AR (June 2023). "Antibiotic strategies for eradicating Pseudomonas aeruginosa in people with cystic fibrosis". The Cochrane Database of Systematic Reviews. 2023 (6): CD004197. doi:10.1002/14651858.CD004197.pub6. PMC 10237531. PMID37268599.
Kuver R, Lee SP (April 2006). "Hypertonic saline for cystic fibrosis". The New England Journal of Medicine. 354 (17): 1848–51, author reply 1848–51. doi:10.1056/NEJMc060351. PMID16642591. S2CID26244542.
Lieberman J (July 1968). "Dornase aerosol effect on sputum viscosity in cases of cystic fibrosis". JAMA. 205 (5): 312–313. doi:10.1001/jama.205.5.312. PMID5694947.
Kellerman D, Rossi Mospan A, Engels J, Schaberg A, Gorden J, Smiley L (August 2008). "Denufosol: a review of studies with inhaled P2Y(2) agonists that led to Phase 3". Pulmonary Pharmacology & Therapeutics. 21 (4): 600–607. doi:10.1016/j.pupt.2007.12.003. PMID18276176.
Wilkinson GR (October 1996). "Cytochrome P4503A (CYP3A) metabolism: prediction of in vivo activity in humans". Journal of Pharmacokinetics and Biopharmaceutics. 24 (5): 475–490. doi:10.1007/BF02353475. PMID9131486. S2CID30289771.
Ferguson JH, Chang AB (May 2014). "Vitamin D supplementation for cystic fibrosis". The Cochrane Database of Systematic Reviews (5): CD007298. doi:10.1002/14651858.CD007298.pub4. PMID24823922.
Huth MM, Zink KA, Van Horn NR (2005). "The effects of massage therapy in improving outcomes for youth with cystic fibrosis: an evidence review". Pediatric Nursing. 31 (4): 328–332. PMID16229132.
Hardin DS, Rice J, Ahn C, Ferkol T, Howenstine M, Spears S, et al. (March 2005). "Growth hormone treatment enhances nutrition and growth in children with cystic fibrosis receiving enteral nutrition". The Journal of Pediatrics. 146 (3): 324–328. doi:10.1016/j.jpeds.2004.10.037. PMID15756212.
Hegarty M, Macdonald J, Watter P, Wilson C (July 2009). "Quality of life in young people with cystic fibrosis: effects of hospitalization, age and gender, and differences in parent/child perceptions". Child. 35 (4): 462–468. doi:10.1111/j.1365-2214.2008.00900.x. PMID18991968. Havermans T, Vreys M, Proesmans M, De Boeck C (January 2006). "Assessment of agreement between parents and children on health-related quality of life in children with cystic fibrosis". Child. 32 (1): 1–7. doi:10.1111/j.1365-2214.2006.00564.x. PMID16398786.
Moorcroft AJ, Dodd ME, Webb AK (1998). "Exercise limitations and training for patients with cystic fibrosis". Disability and Rehabilitation. 20 (6–7): 247–253. doi:10.3109/09638289809166735. PMID9637933.
Rosenstein BJ, Cutting GR (April 1998). "The diagnosis of cystic fibrosis: a consensus statement. Cystic Fibrosis Foundation Consensus Panel". The Journal of Pediatrics. 132 (4): 589–595. doi:10.1016/S0022-3476(98)70344-0. PMID9580754.
Wennberg C, Kucinskas V (1994). "Low frequency of the delta F508 mutation in Finno-Ugrian and Baltic populations". Human Heredity. 44 (3): 169–171. doi:10.1159/000154210. PMID8039801.
Kere J, Savilahti E, Norio R, Estivill X, de la Chapelle A (September 1990). "Cystic fibrosis mutation delta F508 in Finland: other mutations predominate". Human Genetics. 85 (4): 413–415. doi:10.1007/BF02428286. PMID2210753. S2CID38364780.
Gabriel SE, Brigman KN, Koller BH, Boucher RC, Stutts MJ (October 1994). "Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model". Science. 266 (5182): 107–109. Bibcode:1994Sci...266..107G. doi:10.1126/science.7524148. PMID7524148.
Alfonso-Sánchez MA, Pérez-Miranda AM, García-Obregón S, Peña JA (June 2010). "An evolutionary approach to the high frequency of the Delta F508 CFTR mutation in European populations". Medical Hypotheses. 74 (6): 989–992. doi:10.1016/j.mehy.2009.12.018. PMID20110149.
Tobacman JK (June 2003). "Does deficiency of arylsulfatase B have a role in cystic fibrosis?". Chest. 123 (6): 2130–2139. doi:10.1378/chest.123.6.2130. PMID12796199.
Busch R (1990). "On the history of cystic fibrosis". Acta Universitatis Carolinae. Medica. 36 (1–4): 13–15. PMID2130674.
Di Sant'Agnese PA, Darling RC, Perera GA, Shea E (November 1953). "Abnormal electrolyte composition of sweat in cystic fibrosis of the pancreas; clinical significance and relationship to the disease". Pediatrics. 12 (5): 549–563. doi:10.1542/peds.12.5.549. PMID13111855. S2CID42514224.
Eiberg H, Mohr J, Schmiegelow K, Nielsen LS, Williamson R (October 1985). "Linkage relationships of paraoxonase (PON) with other markers: indication of PON-cystic fibrosis synteny". Clinical Genetics. 28 (4): 265–271. doi:10.1111/j.1399-0004.1985.tb00400.x. PMID2998653. S2CID41143417.
Riordan JR, Rommens JM, Kerem B, Alon N, Rozmahel R, Grzelczak Z, et al. (September 1989). "Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA". Science. 245 (4922): 1066–1073. Bibcode:1989Sci...245.1066R. doi:10.1126/science.2475911. PMID2475911. S2CID84566748.
Hanlon GW (August 2007). "Bacteriophages: an appraisal of their role in the treatment of bacterial infections". International Journal of Antimicrobial Agents. 30 (2): 118–128. doi:10.1016/j.ijantimicag.2007.04.006. PMID17566713.
Augarten A, Yahav Y, Kerem BS, Halle D, Laufer J, Szeinberg A, et al. (November 1994). "Congenital bilateral absence of vas deferens in the absence of cystic fibrosis". Lancet. 344 (8935): 1473–1474. doi:10.1016/S0140-6736(94)90292-5. PMID7968122. S2CID28860665.
Gilljam M, Antoniou M, Shin J, Dupuis A, Corey M, Tullis DE (July 2000). "Pregnancy in cystic fibrosis. Fetal and maternal outcome". Chest. 118 (1): 85–91. doi:10.1378/chest.118.1.85. PMID10893364. S2CID32289370.
Edwards QT, Seibert D, Macri C, Covington C, Tilghman J (November 2004). "Assessing ethnicity in preconception counseling: genetics--what nurse practitioners need to know". Journal of the American Academy of Nurse Practitioners. 16 (11): 472–480. doi:10.1111/j.1745-7599.2004.tb00426.x. PMID15617360. S2CID7644129.
Graeber SY, Mall MA (September 2023). "The future of cystic fibrosis treatment: from disease mechanisms to novel therapeutic approaches". Lancet. 402 (10408): 1185–1198. doi:10.1016/s0140-6736(23)01608-2. PMID37699417. S2CID261623275.
Linsdell P (January 2006). "Mechanism of chloride permeation in the cystic fibrosis transmembrane conductance regulator chloride channel". Experimental Physiology. 91 (1): 123–129. doi:10.1113/expphysiol.2005.031757. PMID16157656. S2CID37254079.
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